Neurology:乳突骨瘤与高颅压1例

2019-08-21 杨中华 脑血管病及重症文献导读

54岁,女性。进展性视力丧失和高催乳素血症的表现。

54岁,女性。

进展性视力丧失和高催乳素血症的表现。

头 MRI 显示空蝶鞍(下图 1A),双侧视神经萎缩(下图1B),乳突骨瘤(Mastoid osteoma)(下图2),引起右侧横窦和乙状窦狭窄(下图2B),对侧发育不良:





CSF 压力41 cm H2O,常规检查正常。

临床和影像学提示假瘤脑,也称为特发性高颅压。这个疾病通常与优势的横窦和乙状窦狭窄有关(对侧发育不良)。

原始出处:Gustavo Lima Guarneri, Bernardo Corrêa de Almeida Teixeira. Mastoid osteoma with stenosis of transverse and sigmoid sinuses as a cause of pseudotumor cerebri. Neurology. July 02, 2019;

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Neurology:伴横窦和乙状窦狭窄的乳突骨瘤可致假性脑瘤

54岁女性,表现为进行性视力丧失和高催乳素血症征象,行神经影像学检查,提示部分空蝶鞍(图1A),双侧视神经萎缩(图1B)和扩张性乳突病变(图2),导致右侧横窦和乙状窦狭窄(图2B)。除开放压力增高(41cm H2O)外,脑脊液化验正常。