嗜酸性肉芽肿性多血管炎诊治规范多学科专家共识

2018-07-12 中国风湿免疫科相关专家小组(统称) 中华结核和呼吸杂志, 2018,41(7) : 514-521.

嗜酸性肉芽肿性多血管炎(eosinophilic granulomatosis with polyangiitis,EGPA)是一种可累及全身多个系统的、少见的自身免疫性疾病,主要表现为外周血及组织中嗜酸粒细胞增多、浸润及中小血管的坏死性肉芽肿性炎症,属于抗中性粒细胞胞质抗体(anti-neutrophil cytoplasmic antibodies,ANCA)相关性系统性血管炎。 EGPA可累

中文标题:

嗜酸性肉芽肿性多血管炎诊治规范多学科专家共识

发布日期:

2018-07-12

简要介绍:

嗜酸性肉芽肿性多血管炎(eosinophilic granulomatosis with polyangiitis,EGPA)是一种可累及全身多个系统的、少见的自身免疫性疾病,主要表现为外周血及组织中嗜酸粒细胞增多、浸润及中小血管的坏死性肉芽肿性炎症,属于抗中性粒细胞胞质抗体(anti-neutrophil cytoplasmic antibodies,ANCA)相关性系统性血管炎。 EGPA可累及多系统或器官,由于我国缺乏EGPA大样本的临床数据和资料,不同学科对该病的描述与诊治存在差异。为进一步提高我国各学科对该病的系统认识及临床诊疗水平,由广州呼吸健康研究院钟南山院士、陈荣昌院长及中山大学附属第三医院风湿科古洁若教授牵头,广泛征求国内外多学科专家的意见,同时参考国内外近年来EGPA的研究成果与诊治经验,制定了我国首个EGPA诊治规范多学科专家共识。

拓展指南:血管炎相关指南:

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    2021-07-24 xianglala6

    学习

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