NEJM:眶尖综合征-病例报道

2018-04-26 xing.T MedSci原创

眶尖综合征可能由多种原因引起,包括肿瘤、外伤、炎症和感染。该症状表现为视神经功能障碍合并眼外肌麻痹的视觉障碍。

患者为一名61岁的男子,因右眼眶后疼痛3周和复视、眼睑下垂和视力下降1周而到急诊就诊。

眼科检查显示右眼视力下降(只能感觉到手部运动),相对传入瞳孔缺损,瞳孔反应不良和近乎完全的眼肌麻痹(如图A所示)。角膜、上眼睑和前额的感觉丧失证实了颅神经II、III、VI和V1神经病变。增强的T1加权磁共振成像显示眼球突出伴有眶尖浸润。冠状面(如B图)显示蝶窦之间存在不均匀的液体信号,后者在右侧(箭标)证实含有粘液、血液和坏死物质。眶尖部软组织浸润围绕右侧视神经(虚线圆圈),并在邻近的硬脑膜(箭头)处可见。诊断为右眼眶尖综合征。



眶尖综合征可能由多种原因引起,包括肿瘤、外伤、炎症和感染。该症状表现为视神经功能障碍合并眼外肌麻痹的视觉障碍。

该患者行内镜鼻窦手术并行眶尖减压,获得活检标本。除了用糖皮质激素治疗之外,手术将右眼的视力提高到20/70。活检标本的病理分析显示为高级别弥漫性大B细胞淋巴瘤,并且进一步研究的结果显示广泛转移。开始进行化疗;然而,患者在6周后死亡。

原始出处:

Nicole A. Borchard,et al. Orbital Apex Syndrome. N Engl J Med 2018; http://www.nejm.org/doi/full/10.1056/NEJMicm1703770

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createdName=jihuaijun1112, createdTime=Sat Apr 28 07:33:36 CST 2018, time=2018-04-28, status=1, ipAttribution=), GetPortalCommentsPageByObjectIdResponse(id=1431198, encodeId=4ba01431198dc, content=<a href='/topic/show?id=f9b9e9124a8' target=_blank style='color:#2F92EE;'>#综合征#</a>, beContent=null, objectType=article, channel=null, level=null, likeNumber=31, replyNumber=0, topicName=null, topicId=null, topicList=[TopicDto(id=79124, encryptionId=f9b9e9124a8, topicName=综合征)], attachment=null, authenticateStatus=null, createdAvatar=https://wx.qlogo.cn/mmopen/aLGWoFXAyMbIu3qymFOyheQLjPSX3OUs5GmkyBlcCOwTPIeq3why9NGibxxUqYo6hcx8qZLHZFgNPnBK1yzWeOFpyg2OnWOt0/0, createdBy=fa4716, createdName=zhouqu_8, createdTime=Sat Apr 28 00:10:00 CST 2018, time=2018-04-28, status=1, ipAttribution=)]
    2018-05-02 jihuaijun1112

    学习学习学习

    0

  4. 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createdName=jihuaijun1112, createdTime=Sat Apr 28 07:33:36 CST 2018, time=2018-04-28, status=1, ipAttribution=), GetPortalCommentsPageByObjectIdResponse(id=1431198, encodeId=4ba01431198dc, content=<a href='/topic/show?id=f9b9e9124a8' target=_blank style='color:#2F92EE;'>#综合征#</a>, beContent=null, objectType=article, channel=null, level=null, likeNumber=31, replyNumber=0, topicName=null, topicId=null, topicList=[TopicDto(id=79124, encryptionId=f9b9e9124a8, topicName=综合征)], attachment=null, authenticateStatus=null, createdAvatar=https://wx.qlogo.cn/mmopen/aLGWoFXAyMbIu3qymFOyheQLjPSX3OUs5GmkyBlcCOwTPIeq3why9NGibxxUqYo6hcx8qZLHZFgNPnBK1yzWeOFpyg2OnWOt0/0, createdBy=fa4716, createdName=zhouqu_8, createdTime=Sat Apr 28 00:10:00 CST 2018, time=2018-04-28, status=1, ipAttribution=)]
    2018-05-02 jihuaijun1112

    学习学习学习

    0

  5. 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createdName=jihuaijun1112, createdTime=Sat Apr 28 07:33:36 CST 2018, time=2018-04-28, status=1, ipAttribution=), GetPortalCommentsPageByObjectIdResponse(id=1431198, encodeId=4ba01431198dc, content=<a href='/topic/show?id=f9b9e9124a8' target=_blank style='color:#2F92EE;'>#综合征#</a>, beContent=null, objectType=article, channel=null, level=null, likeNumber=31, replyNumber=0, topicName=null, topicId=null, topicList=[TopicDto(id=79124, encryptionId=f9b9e9124a8, topicName=综合征)], attachment=null, authenticateStatus=null, createdAvatar=https://wx.qlogo.cn/mmopen/aLGWoFXAyMbIu3qymFOyheQLjPSX3OUs5GmkyBlcCOwTPIeq3why9NGibxxUqYo6hcx8qZLHZFgNPnBK1yzWeOFpyg2OnWOt0/0, createdBy=fa4716, createdName=zhouqu_8, createdTime=Sat Apr 28 00:10:00 CST 2018, time=2018-04-28, status=1, ipAttribution=)]
    2018-05-01 jihuaijun1112

    学习学习学习

    0

  6. 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createdName=jihuaijun1112, createdTime=Sat Apr 28 07:33:36 CST 2018, time=2018-04-28, status=1, ipAttribution=), GetPortalCommentsPageByObjectIdResponse(id=1431198, encodeId=4ba01431198dc, content=<a href='/topic/show?id=f9b9e9124a8' target=_blank style='color:#2F92EE;'>#综合征#</a>, beContent=null, objectType=article, channel=null, level=null, likeNumber=31, replyNumber=0, topicName=null, topicId=null, topicList=[TopicDto(id=79124, encryptionId=f9b9e9124a8, topicName=综合征)], attachment=null, authenticateStatus=null, createdAvatar=https://wx.qlogo.cn/mmopen/aLGWoFXAyMbIu3qymFOyheQLjPSX3OUs5GmkyBlcCOwTPIeq3why9NGibxxUqYo6hcx8qZLHZFgNPnBK1yzWeOFpyg2OnWOt0/0, createdBy=fa4716, createdName=zhouqu_8, createdTime=Sat Apr 28 00:10:00 CST 2018, time=2018-04-28, status=1, ipAttribution=)]
    2018-04-30 jihuaijun1112

    学习学习学习

    0

  7. 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    2018-04-30 jihuaijun1112

    学习学习学习学习

    0

  8. 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createdName=jihuaijun1112, createdTime=Sat Apr 28 07:33:36 CST 2018, time=2018-04-28, status=1, ipAttribution=), GetPortalCommentsPageByObjectIdResponse(id=1431198, encodeId=4ba01431198dc, content=<a href='/topic/show?id=f9b9e9124a8' target=_blank style='color:#2F92EE;'>#综合征#</a>, beContent=null, objectType=article, channel=null, level=null, likeNumber=31, replyNumber=0, topicName=null, topicId=null, topicList=[TopicDto(id=79124, encryptionId=f9b9e9124a8, topicName=综合征)], attachment=null, authenticateStatus=null, createdAvatar=https://wx.qlogo.cn/mmopen/aLGWoFXAyMbIu3qymFOyheQLjPSX3OUs5GmkyBlcCOwTPIeq3why9NGibxxUqYo6hcx8qZLHZFgNPnBK1yzWeOFpyg2OnWOt0/0, createdBy=fa4716, createdName=zhouqu_8, createdTime=Sat Apr 28 00:10:00 CST 2018, time=2018-04-28, status=1, ipAttribution=)]
    2018-04-28 jihuaijun1112

    ****学习学习学习.

    0

  9. 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createdName=jihuaijun1112, createdTime=Sat Apr 28 07:33:36 CST 2018, time=2018-04-28, status=1, ipAttribution=), GetPortalCommentsPageByObjectIdResponse(id=1431198, encodeId=4ba01431198dc, content=<a href='/topic/show?id=f9b9e9124a8' target=_blank style='color:#2F92EE;'>#综合征#</a>, beContent=null, objectType=article, channel=null, level=null, likeNumber=31, replyNumber=0, topicName=null, topicId=null, topicList=[TopicDto(id=79124, encryptionId=f9b9e9124a8, topicName=综合征)], attachment=null, authenticateStatus=null, createdAvatar=https://wx.qlogo.cn/mmopen/aLGWoFXAyMbIu3qymFOyheQLjPSX3OUs5GmkyBlcCOwTPIeq3why9NGibxxUqYo6hcx8qZLHZFgNPnBK1yzWeOFpyg2OnWOt0/0, createdBy=fa4716, createdName=zhouqu_8, createdTime=Sat Apr 28 00:10:00 CST 2018, time=2018-04-28, status=1, ipAttribution=)]
    2018-04-28 jihuaijun1112

    学习学习学习.

    0

  10. 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