Neurology:眼-腭肌阵挛:脑干损伤的可能后果

2019-01-31 zyx整理 神经科病例撷英拾粹

61岁男性,既往有左侧小脑梗死,主诉卒中后视物成双伴头晕数月。

61岁男性,既往有左侧小脑梗死,主诉卒中后视物成双伴头晕数月。脑梗死如图所示。查体提示所有方向凝视均可见旋转性眼球震颤,左侧凝视时明显(视频1)。口部检查可见腭肌震颤(视频2)。眼-腭震颤(Oculopalatal tremor,OPT)被认为是由于红核(中脑),齿状核(小脑)和下橄榄核(延髓)之间的连接中断所致。最常见的原因是脑干梗死或出血,但也可在多发性硬化和其他炎症性疾病中观察到。OPT通常在脑干损伤几个月后较为明显。治疗可包括加巴喷丁,美金刚,苯二氮卓类药物和丙戊酸。

(图:可见累及左侧小脑半球尾部的脑梗死;受累部位对应于小脑后下动脉供血区)

(所有方向凝视均可见朝向左侧的旋转性眼球震颤,但往左侧和上方凝视时更明显;低剂量氯硝西泮可使旋转性眼球震颤的幅度和频率得到改善)

(可见软腭节律性收缩)

原始出处:Lawal O, Fisayo A. Teaching Video NeuroImages: Oculopalatal myoclonus: A possible consequence of brainstem injury. Neurology. 2018 Nov 27;91(22):e2104-e2105.

版权声明:
本网站所有内容来源注明为“梅斯医学”或“MedSci原创”的文字、图片和音视频资料,版权均属于梅斯医学所有。非经授权,任何媒体、网站或个人不得转载,授权转载时须注明来源为“梅斯医学”。其它来源的文章系转载文章,或“梅斯号”自媒体发布的文章,仅系出于传递更多信息之目的,本站仅负责审核内容合规,其内容不代表本站立场,本站不负责内容的准确性和版权。如果存在侵权、或不希望被转载的媒体或个人可与我们联系,我们将立即进行删除处理。
在此留言
评论区 (3)
#插入话题
  1. [GetPortalCommentsPageByObjectIdResponse(id=2000690, encodeId=098d2000690fa, content=<a href='/topic/show?id=d5df12695e6' target=_blank style='color:#2F92EE;'>#Neurol#</a>, beContent=null, objectType=article, channel=null, level=null, likeNumber=38, replyNumber=0, topicName=null, topicId=null, topicList=[TopicDto(id=12695, encryptionId=d5df12695e6, topicName=Neurol)], attachment=null, authenticateStatus=null, createdAvatar=, createdBy=8217292, createdName=yinhl1978, createdTime=Fri Jul 26 15:36:00 CST 2019, time=2019-07-26, status=1, ipAttribution=), GetPortalCommentsPageByObjectIdResponse(id=1984228, encodeId=84e919842284e, content=<a href='/topic/show?id=420681092f7' target=_blank style='color:#2F92EE;'>#肌阵挛#</a>, beContent=null, objectType=article, channel=null, level=null, likeNumber=74, replyNumber=0, topicName=null, topicId=null, topicList=[TopicDto(id=81092, encryptionId=420681092f7, topicName=肌阵挛)], attachment=null, authenticateStatus=null, createdAvatar=, createdBy=5eee468, createdName=zxl729, createdTime=Tue Sep 17 22:36:00 CST 2019, time=2019-09-17, status=1, ipAttribution=), GetPortalCommentsPageByObjectIdResponse(id=1397709, encodeId=fbd4139e709d4, content=<a href='/topic/show?id=8bee565436d' target=_blank style='color:#2F92EE;'>#损伤#</a>, beContent=null, objectType=article, channel=null, level=null, likeNumber=42, replyNumber=0, topicName=null, topicId=null, topicList=[TopicDto(id=56543, encryptionId=8bee565436d, topicName=损伤)], attachment=null, authenticateStatus=null, createdAvatar=https://thirdwx.qlogo.cn/mmopen/vi_32/DYAIOgq83eoNX3lUOlDKGBUEPNwZx0nibmdcFyeibnX4WMhUSCU2REpGRWtSmnT2CCs0dA5waxvJknYDxwtYnIcQ/132, createdBy=294e2500218, createdName=ms3046638856685384, createdTime=Sat Feb 02 13:36:00 CST 2019, time=2019-02-02, status=1, ipAttribution=)]
    2019-07-26 yinhl1978
  2. [GetPortalCommentsPageByObjectIdResponse(id=2000690, encodeId=098d2000690fa, content=<a href='/topic/show?id=d5df12695e6' target=_blank style='color:#2F92EE;'>#Neurol#</a>, beContent=null, objectType=article, channel=null, level=null, likeNumber=38, replyNumber=0, topicName=null, topicId=null, topicList=[TopicDto(id=12695, encryptionId=d5df12695e6, topicName=Neurol)], attachment=null, authenticateStatus=null, createdAvatar=, createdBy=8217292, createdName=yinhl1978, createdTime=Fri Jul 26 15:36:00 CST 2019, time=2019-07-26, status=1, ipAttribution=), GetPortalCommentsPageByObjectIdResponse(id=1984228, encodeId=84e919842284e, content=<a href='/topic/show?id=420681092f7' target=_blank style='color:#2F92EE;'>#肌阵挛#</a>, beContent=null, objectType=article, channel=null, level=null, likeNumber=74, replyNumber=0, topicName=null, topicId=null, topicList=[TopicDto(id=81092, encryptionId=420681092f7, topicName=肌阵挛)], attachment=null, authenticateStatus=null, createdAvatar=, createdBy=5eee468, createdName=zxl729, createdTime=Tue Sep 17 22:36:00 CST 2019, time=2019-09-17, status=1, ipAttribution=), GetPortalCommentsPageByObjectIdResponse(id=1397709, encodeId=fbd4139e709d4, content=<a href='/topic/show?id=8bee565436d' target=_blank style='color:#2F92EE;'>#损伤#</a>, beContent=null, objectType=article, channel=null, level=null, likeNumber=42, replyNumber=0, topicName=null, topicId=null, topicList=[TopicDto(id=56543, encryptionId=8bee565436d, topicName=损伤)], attachment=null, authenticateStatus=null, createdAvatar=https://thirdwx.qlogo.cn/mmopen/vi_32/DYAIOgq83eoNX3lUOlDKGBUEPNwZx0nibmdcFyeibnX4WMhUSCU2REpGRWtSmnT2CCs0dA5waxvJknYDxwtYnIcQ/132, createdBy=294e2500218, createdName=ms3046638856685384, createdTime=Sat Feb 02 13:36:00 CST 2019, time=2019-02-02, status=1, ipAttribution=)]
    2019-09-17 zxl729
  3. [GetPortalCommentsPageByObjectIdResponse(id=2000690, encodeId=098d2000690fa, content=<a href='/topic/show?id=d5df12695e6' target=_blank style='color:#2F92EE;'>#Neurol#</a>, beContent=null, objectType=article, channel=null, level=null, likeNumber=38, replyNumber=0, topicName=null, topicId=null, topicList=[TopicDto(id=12695, encryptionId=d5df12695e6, topicName=Neurol)], attachment=null, authenticateStatus=null, createdAvatar=, createdBy=8217292, createdName=yinhl1978, createdTime=Fri Jul 26 15:36:00 CST 2019, time=2019-07-26, status=1, ipAttribution=), GetPortalCommentsPageByObjectIdResponse(id=1984228, encodeId=84e919842284e, content=<a href='/topic/show?id=420681092f7' target=_blank style='color:#2F92EE;'>#肌阵挛#</a>, beContent=null, objectType=article, channel=null, level=null, likeNumber=74, replyNumber=0, topicName=null, topicId=null, topicList=[TopicDto(id=81092, encryptionId=420681092f7, topicName=肌阵挛)], attachment=null, authenticateStatus=null, createdAvatar=, createdBy=5eee468, createdName=zxl729, createdTime=Tue Sep 17 22:36:00 CST 2019, time=2019-09-17, status=1, ipAttribution=), GetPortalCommentsPageByObjectIdResponse(id=1397709, encodeId=fbd4139e709d4, content=<a href='/topic/show?id=8bee565436d' target=_blank style='color:#2F92EE;'>#损伤#</a>, beContent=null, objectType=article, channel=null, level=null, likeNumber=42, replyNumber=0, topicName=null, topicId=null, topicList=[TopicDto(id=56543, encryptionId=8bee565436d, topicName=损伤)], attachment=null, authenticateStatus=null, createdAvatar=https://thirdwx.qlogo.cn/mmopen/vi_32/DYAIOgq83eoNX3lUOlDKGBUEPNwZx0nibmdcFyeibnX4WMhUSCU2REpGRWtSmnT2CCs0dA5waxvJknYDxwtYnIcQ/132, createdBy=294e2500218, createdName=ms3046638856685384, createdTime=Sat Feb 02 13:36:00 CST 2019, time=2019-02-02, status=1, ipAttribution=)]

相关资讯

Med Sci Monit:羟考酮预处理能同时减少快速顺序麻醉诱导中依托咪酯诱发的肌阵挛和罗库溴铵诱发的回避反应

依托咪酯和罗库溴铵通常被同时用于快速顺序诱导麻醉。然而,羟考酮预处理对肌阵挛和回避反应的影响并没有文献报道。本研究的目的是评估羟考酮预处理对快速顺序诱导麻醉中依托咪酯诱发的肌阵挛和罗库溴铵诱发的回避反应的发生率和严重程度的影响。

Lancet Neurol:抗GABAA受体脑炎常伴癫痫持续状态

越来越多的证据显示癫痫发作及癫痫持续状态可由免疫介导。该研究通过分析一类新的癫痫综合征系列临床表现,探索此类疾病的靶抗原及患者体内抗体对神经细胞的影响。 此为观察性研究,提取140例出现脑炎、癫痫发作或癫痫持续状态的患者血清及脑脊液标本,分析抗原特性及未明神经纤维抗原相关抗体。样本来源于2006年4月28日至2013年4月25日期间世界各国研究中心怀疑为自身免疫性脑炎的患者。以75例健康

Neurology:Unverricht-Lundborg病病程以及进展因素研究

研究发现,确诊年龄越早,发生严重肌阵挛的时间越早,持续性癫痫是疾病症状加重的预测指标

引以为戒!一例肌阵挛失神癫痫治疗失败引发的思考

肌阵挛性失神性癫痫(Epilepsy with Myoclonic absences,EMA)是一种以肌阵挛性失神(Myoclonic absences, MA)为主要发作类型的少见的儿童癫痫综合征。