Lung Involvement in Destombes-Rosai-Dorfman Disease Clinical and Radiological Features and Response to the MEK Inhibitor Cobimetinib

Moyon, Q; Boussouar, S; Maksud, P; Emile, JF; Charlotte, F; Aladjidi, N; Prevot, G; Donadieu, J; Amoura, Z; Grenier, P; Haroche, J; Aubart, FC

Aubart, FC (corresponding author), Grp Hosp Pitie Salpetriere, Inst E3m, Serv Med Interne 2, 47-83 Blvd Hop, F-75651 Paris 13, France.

CHEST, 2020; 157 (2): 323

Abstract

BACKGROUND: Destombes-Rosai-Dorfman disease (RDD) is a rare multisystemic histiocytosis. Pulmonary involvement during RDD has been poorly described. T......

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