Sweat rate analysis of ivacaftor potentiation of CFTR in non-CF adults

Kim, J; Farahmand, M; Dunn, C; Milla, CE; Horii, RI; Thomas, EAC; Moss, RB; Wine, JJ

Wine, JJ (reprint author), Stanford Univ, Cyst Fibrosis Res Lab, Stanford, CA 94305 USA.; Wine, JJ (reprint author), Stanford Univ, Dept Pediat, Sch Med, Stanford, CA 94305 USA.; Wine, JJ (reprint author), Stanford Univ, Dept Psychol, Stanford, CA 94305 U

SCIENTIFIC REPORTS, 2018; 8 ():

Abstract

To determine if ivacaftor (Kalydeco) influences non-CF human CFTR function in vivo, we measured CFTR-dependent (C-sweat) and CFTR-independent (M-sweat......

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