中国半侧颜面短小畸形·下颌骨畸形临床诊疗指南

2018-01-30 中华医学会肿瘤学分会 中华整形外科杂志,2018,34(1) :1-5.

半侧颜面短小畸形(hemifacial microsomia,HFM)是一种以半侧面部多种组织结构发育不良为特点的先天性疾病,偶见于双侧,主要表现为颅面骨、耳廓及面部软组织发育不良,发病率约为(1.8~2.9)/10000,是常见的重大体表出生缺陷之一。该疾病不仅造成严重的面部畸形,还伴随呼吸、进食、语言、听力等功能障碍及心理障碍,严重影响患者的生活质量,给患者及其家庭带来极大痛苦和经济负担,需要

中文标题:

中国半侧颜面短小畸形·下颌骨畸形临床诊疗指南

发布日期:

2018-01-30

简要介绍:

半侧颜面短小畸形(hemifacial microsomia,HFM)是一种以半侧面部多种组织结构发育不良为特点的先天性疾病,偶见于双侧,主要表现为颅面骨、耳廓及面部软组织发育不良,发病率约为(1.8~2.9)/10000,是常见的重大体表出生缺陷之一。该疾病不仅造成严重的面部畸形,还伴随呼吸、进食、语言、听力等功能障碍及心理障碍,严重影响患者的生活质量,给患者及其家庭带来极大痛苦和经济负担,需要长期多学科联合治疗。

HFM曾被称为:半侧颜面发育不全、第一二鳃弓综合征、口-下颌-耳综合征、单侧颜面发育不全、口下颌骨发育障碍、颅面短小畸形、先天性耳颅综合征等,为避免混淆,现统一命名为半侧颜面短小畸形,英文名称为:Hemifacial Microsomia。

 

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    2018-03-30 1e16d8a5m40(暂无匿称)

    学习了

    0

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    2018-03-04 龙胆草

    学习谢谢分享

    0

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    2018-02-17 有备才能无患

    半侧颜面短小畸形(hemifacial microsomia.HFM)是一种以半侧面部多种组织结构发育不良为特点的先天性疾病.偶见于双侧.主要表现为颅面骨.耳廓及面部软组织发育不良.发病率约为(1.8-2.9)/10000.是常见的重大体表出生缺陷之一.该疾病不仅造成严重的面部畸形.还伴随呼吸.进食.语言.听力等功能障碍及心理障碍.严重影响患者的生活质量.给患者及其家庭带来极大痛苦和经济负担.需要长期多学科联合治疗.?

    0