后纵隔巨大椎管相关性节细胞神经瘤1例

2018-03-16 佚名 医学影像学杂志

患者女,23岁。

【一般资料】

患者女,23岁。

【主诉】

1年前无明显原因反复阵发性咳嗽伴黄痰,无高热、盗汗。

【现病史】

2月前咳嗽、咳痰加重,痰中带血丝。心脏彩超示:先天性心脏病(房间隔缺损Ⅱ型)。

【辅助检查】

术前CT平扫可见后纵隔右侧脊柱旁及脊柱前软组织肿块影,呈梭形以胸9为中心上下径约19cm,最大横径约10cm×6cm。肿块向下延伸至腹膜后。肿块内可见少量斑点状钙化影,多个椎体及肋骨呈侵蚀性骨质破坏,且多个椎间孔扩大。CT三期增强扫描肿块呈轻度强化,延时期强化比动脉期及静脉期略明显(CT值平均增加约9HU)。MRI示肿块在T1WI呈等信号,T2WI和T2WI压脂序列呈不均匀稍高信号。肿块通过多个椎间孔侵入椎管内,局部脊髓受压移位。肿块推移下腔静脉向前移位。MR增强扫描肿块呈轻度不均匀斑片状强化。经胸腔穿刺病理活检:穿刺组织中见神经纤维增生,结构紊乱,血管丰富,部分区见神经节细胞。



【初步诊断

后纵隔脊柱旁节细胞神经瘤。

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