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LYMPHATIC SYSTEM MALFORMATIONS IN NOONAN SYNDROME: TWO CASE REPORTS AND IMAGING ANALYSIS

期刊: LYMPHOLOGY, 2020; 53 (2)

Lymphedema is a well-known complication of Noonan syndrome (NS) but the lymphatic malformations in NS are poorly understood. We report clinical, genet......

INCREASED TRAFFICKING OF MESENTERIC LYMPH-DERIVED gamma delta T CELLS INTO INTESTINAL MUCOSA IS ASSOCIATED WITH GUT INJURY AFTER INTESTINAL ISCHEMIA-REPERFUSION IN RATS

期刊: LYMPHOLOGY, 2019; 52 (2)

We sought to investigate the effects of mesenteric lymph-derived gamma delta T cells trafficking into intestinal mucosa on gut injury after intestinal......

JIF:0.67

A LYVE-1/CRSBP-1 MUTATION IN INHERITED PRIMARY LYMPHEDEMA

期刊: LYMPHOLOGY, 2017; 50 (1)

Primary lymphedema is clinically and genetically heterogeneous with germline mutations identified in approximately 20 primary lymphedema genes. The ly......

JIF:0.98

TRANSDIFFERENTIATED MONOCYTES: A NOVEL SOURCE OF LYMPHATIC ENDOTHELIAL-LIKE CELLS

期刊: LYMPHOLOGY, 2017; 50 (2)

Although monocytes have previously been demonstrated to contribute to lymphatic vessel formation in vivo, monocyte transdifferentiation into lymphatic......

JIF:0.98

MULTI-MODAL IMAGING FEATURES AND LYMPHO-VENOUS SHUNT FOR VAGINAL CHYLOUS FISTULA IN LYMPHANGIOLEIOMYOMATOSIS: CASE-REPORT AND REVIEW

期刊: LYMPHOLOGY, 2017; 50 (3)

Vaginal chylous fistula is a very rare lymphatic disorder and lymphangioleiomyomatosis (LAM) is also a rare multisystemic disease. LAM with the develo......

JIF:0.98

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