C1-inhibitor/C1-inhibitor antibody complexes in acquired angioedema due to C1-inhibitor deficiency

Polai, Z; Kajdacsi, E; Cervenak, L; Balla, Z; Benedek, S; Varga, L; Farkas, H

Farkas, H (通讯作者),Semmelweis Univ, Hungarian Angioedema Ctr Reference & Excellence, Dept Internal Med & Haematol, Szentkiraly U 46, H-1088 Budapest, Hungary.

ORPHANET JOURNAL OF RARE DISEASES, 2023; 18 (1):

Abstract

BackgroundAutoantibodies against C1-inhibitor (C1-INH-Ab) have a diagnostic value in acquired angioedema due to C1-inhibitor deficiency (C1-INH-AAE), ......

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