Hemophagocytic syndrome triggered by intense physical activity and viral infection in a young adult female with three heterozygous mutations in Munc-18-2

Markovic, O; Janic, D; Pavlovic, M; Tukic, L; Jankovic, S; Filipovic, B; Marisavljevic, D

Markovic, O (reprint author), Clin Hosp Ctr Bezanijska Kosa Bezanijska Kosa Bb, Belgrade 11000, Serbia.

VOJNOSANITETSKI PREGLED, 2017; 74 (5): 494

Abstract

Introduction. Hemophagocytic lymphohistiocytosis (HLH) is a rare, potentially life-threatening, hyperinflammatory syndrome caused by severe hypercytok......

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