Odd- and even-numbered medium-chained fatty acids protect against glutathione depletion in very long-chain acyl-CoA dehydrogenase deficiency

Lund, M; Heaton, R; Hargreaves, IP; Gregersen, N; Olsen, RKJ

Lund, M; Olsen, RKJ (通讯作者),Aarhus Univ, Aarhus Univ Hosp, Dept Clin Med, Res Unit Mol Med, Palle Juel Jensens Blvd 99, DK-8200 Aarhus, Denmark.

BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR AND CELL BIOLOGY OF LIPIDS, 2023; 1868 (2):

Abstract

Recent trials have reported the ability of triheptanoin to improve clinical outcomes for the severe symptoms associated with long-chain fatty acid oxi......

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