Disruption of mitochondrial functions involving mitochondrial permeability transition pore opening caused by maleic acid in rat kidney

Roginski, AC; Zemniacak, AB; Marschner, RA; Wajner, SM; Ribeiro, RT; Wajner, M; Amaral, AU

Amaral, AU (通讯作者),Univ Fed Rio Grande Do Sul, Inst Ciencias Basicas Saude, Programa Posgrad Ciencias Biol Bioquim, Porto Alegre, RS, Brazil.;Amaral, AU (通讯作者),Univ Reg Integrada Alto Uruguai & Missoes, Dept Ciencias Biol, Ave Sete Setembro 1621, BR-99709910 Erechim, RS, Brazil.

JOURNAL OF BIOENERGETICS AND BIOMEMBRANES, 2022; 54 (4): 203

Abstract

Propionic acid (PA) predominantly accumulates in tissues and biological fluids of patients affected by propionic acidemia that may manifest chronic re......

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