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先天性巨结肠的诊断及治疗专家共识

2017-12-14 中华医学会小儿外科学分会 中华小儿外科杂志,2017,38(11) :805-815.

先天性巨结肠诊断

先天性巨结肠(Hirschsprung’s disease，HSCR)是一种常见的肠神经元发育异常性疾病，发病率约为1/5 000，男性发病率是女性的4倍。HSCR的病理学改变主要是狭窄段肌间神经丛和黏膜下神经丛内神经节细胞缺如，但外源性神经纤维增粗、数目增多。根据无神经节细胞肠段的范围，HSCR的临床分型包括：①短段型：指狭窄段位于直肠中、远段；②常见型：又称普通型，指狭窄段位于肛门至直肠近端或

中文标题：

先天性巨结肠的诊断及治疗专家共识

发布机构：

中华医学会小儿外科学分会

发布日期：

2017-12-14

简要介绍：

先天性巨结肠(Hirschsprung’s disease，HSCR)是一种常见的肠神经元发育异常性疾病，发病率约为1/5 000，男性发病率是女性的4倍。HSCR的病理学改变主要是狭窄段肌间神经丛和黏膜下神经丛内神经节细胞缺如，但外源性神经纤维增粗、数目增多。根据无神经节细胞肠段的范围，HSCR的临床分型包括：①短段型：指狭窄段位于直肠中、远段；②常见型：又称普通型，指狭窄段位于肛门至直肠近端或直肠乙状结肠交界处，甚至达乙状结肠远端；③长段型：指狭窄段自肛门延至降结肠甚至横结肠；④全结肠型：指狭窄段波及升结肠及距回盲部30 cm以内的回肠；⑤全肠型：指狭窄段波及全部结肠及距回盲部30cm以上小肠，甚至累及十二指肠。

 

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    2021-07-05 shirly.li19560809

    很有用

    0

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    2018-02-06 12198cffm94(暂无昵称)

    学习

    0

  3. [GetPortalCommentsPageByObjectIdResponse(id=996549, encodeId=2d2b996549ed, content=很有用, beContent=null, objectType=guider, channel=null, level=null, likeNumber=46, replyNumber=0, topicName=null, topicId=null, topicList=[], attachment=null, authenticateStatus=null, createdAvatar=, createdBy=f72b1400629, createdName=shirly.li19560809, createdTime=Mon Jul 05 21:15:45 CST 2021, time=2021-07-05, status=1, ipAttribution=), GetPortalCommentsPageByObjectIdResponse(id=285711, encodeId=65dc285e1143, content=学习, beContent=null, objectType=guider, channel=null, level=null, likeNumber=60, replyNumber=0, topicName=null, topicId=null, topicList=[], attachment=null, authenticateStatus=null, createdAvatar=, createdBy=662c2267356, createdName=12198cffm94(暂无昵称), createdTime=Tue Feb 06 20:11:04 CST 2018, time=2018-02-06, status=1, ipAttribution=), GetPortalCommentsPageByObjectIdResponse(id=270751, encodeId=57302e07514f, content=一起学习学习, beContent=null, objectType=guider, channel=null, level=null, likeNumber=51, replyNumber=0, topicName=null, topicId=null, topicList=[], attachment=null, authenticateStatus=null, createdAvatar=https://wx.qlogo.cn/mmopen/vi_32/TDiaAWyicHgedzX3wKo3qcxudVJib7AfibfvNeufHRF2jG3Bw8MmZyWjIhtBV1mpJI7Sy9n7RcBKK5t3CuOKuOFxkg/0, createdBy=dd702206933, createdName=wzb521zf, createdTime=Wed Dec 20 01:02:02 CST 2017, time=2017-12-20, status=1, ipAttribution=), GetPortalCommentsPageByObjectIdResponse(id=270586, encodeId=f5f12e05864d, content=学习, beContent=null, objectType=guider, channel=null, level=null, likeNumber=61, replyNumber=0, topicName=null, topicId=null, topicList=[], attachment=null, authenticateStatus=null, createdAvatar=http://thirdwx.qlogo.cn/mmopen/vi_32/Q0j4TwGTfTJpBl6xwMmnsKibwxcAIltOH3nnCEQbNE6TDbYtCKe8hYI0oJrbduNqnJraM1PyyjPKU1suAzicYPaA/132, createdBy=eeaf2031798, createdName=海之蓝, createdTime=Tue Dec 19 09:58:27 CST 2017, time=2017-12-19, status=1, ipAttribution=), GetPortalCommentsPageByObjectIdResponse(id=269450, encodeId=3f97269450f7, content=先天性巨结肠(Hirschsprung`s disease.HSCR)是一种常见的肠神经元发育异常性疾病.发病率约为1/5 000.男性发病率是女性的4倍., beContent=null, objectType=guider, channel=null, level=null, likeNumber=68, replyNumber=0, topicName=null, topicId=null, topicList=[], attachment=null, authenticateStatus=null, createdAvatar=https://wx.qlogo.cn/mmopen/NUyjXTCJjo7cJ6ejWUr2nIia8qOvAKNdLHr32Df6G8iaoaOx6pHaoiacwp26DaslxZHCGbibZhhCGven4rvmWP60GahtzgFjgCjR/0, createdBy=6b111703011, createdName=有备才能无患, createdTime=Thu Dec 14 23:18:29 CST 2017, time=2017-12-14, status=1, ipAttribution=)]
    2017-12-20 wzb521zf

    一起学习学习

    0

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    2017-12-19 海之蓝

    学习

    0

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    2017-12-14 有备才能无患

    先天性巨结肠(Hirschsprung`s disease.HSCR)是一种常见的肠神经元发育异常性疾病.发病率约为1/5 000.男性发病率是女性的4倍.

    0

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